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Pregnancy in complex CHD: focus on patients with Fontan circulation and patients with a systemic right ventricle*

Published online by Cambridge University Press:  16 December 2015

Abigail Khan  and
Yuli Y. Kim
Abigail Khan
Affiliation:
Philadelphia Adult Congenital Heart Center, Perelman School of Medicine at the University of Pennsylvania Philadelphia, Pennsylvania, United States of America
Yuli Y. Kim*
Affiliation:
Philadelphia Adult Congenital Heart Center, Perelman School of Medicine at the University of Pennsylvania Philadelphia, Pennsylvania, United States of America
*
Correspondence to: Dr Y.Y. Kim, MD, Philadelphia Adult Congenital Heart Center, Perelman School of Medicine at the University of Pennsylvania Philadelphia, PA 19104, United States of America. Tel: 215-615-3388; Fax: 215-349-5927; E-mail: kimy@email.chop.edu
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Abstract

The majority of children with congenital heart disease (CHD) now survive into adulthood, and many women with CHD want to pursue pregnancy. Pregnancy represents a complex issue for the CHD care provider. It requires balancing the interests of the woman against the risk to her health during pregnancy, while also factoring in the long-term risks to her health and the risk to her fetus. Our knowledge about this subject has been historically limited by lack of data regarding the outcome of pregnancy in CHD; however, in recent years, more data have begun to emerge. In this review, we will summarise what is known about risk assessment in pregnant CHD patients. We provide a framework for healthcare providers managing pregnancy in this population, with focus on the systemic right ventricle and the Fontan operation.

Keywords

Pregnancycongenital heart diseaserisk assessment
Type
Original Articles
Information
Cardiology in the Young , Volume 25 , Issue 8: HeartWeek 2015 , December 2015 , pp. 1608 - 1614
Copyright
© Cambridge University Press 2015 

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Footnotes

*

Presented at the Children’s Hospital of Philadelphia Cardiology 2015: 18th Annual Update on Pediatric and Congenital Cardiovascular Disease: “Challenges and Dilemmas”, Scottsdale, Arizona, United States of America, Wednesday February 11, 2015 – Sunday, February 15, 2015.

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