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Divided left atrium with obstruction of pulmonary venous return in the setting of hypoplasia of the left heart

Published online by Cambridge University Press:  21 January 2005

Sara E. Monaco ,
Welton M. Gersony  and
Harshwardhan M. Thaker
Sara E. Monaco
Affiliation:
Department of Pathology, Columbia University Medical Center, New York, NY, USA
Welton M. Gersony
Affiliation:
Department of Pathology, Columbia University Medical Center, New York, NY, USA
Harshwardhan M. Thaker
Affiliation:
Department of Pathology, Columbia University Medical Center, New York, NY, USA
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Abstract

We describe an infant with hypoplasia of the left heart diagnosed prenatally who, at birth, had signs of severe pulmonary venous obstruction. Echocardiography indicated normally connecting pulmonary veins, and showed a paradoxical right-to-left shunt across a patent oval foramen. Postmortem examination revealed that the obstruction was due to a divided left atrium, or cor triatriatum sinister, with an imperforate muscular diaphragm separating completely the two components of the divided atrium.

Keywords

Cor triatriatumanomalous pulmonary venous returncommon pulmonary venous atresiaalveolar capillary dysplasiamisaligned veinspulmonary lymphangiectasia
Type
Brief Report
Information
Cardiology in the Young , Volume 14 , Issue 5 , October 2004 , pp. 553 - 556
Copyright
© 2004 Cambridge University Press

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