Case report
Torsed reactive nodular fibrous pseudotumor in an adolescent: case report and review of the literature

https://doi.org/10.1016/j.jpedsurg.2012.01.001Get rights and content

Abstract

We describe a case of a 13-year-old girl presenting with acute abdominal pain and imaging suggesting acute appendicitis. Upon laparoscopy, she was found to have a mass attached to the jejunum that had torsed upon its blood supply. On histopathologic studies, the mass was determined to be a reactive nodular fibrous pseudotumor. This lesion is a benign neoplasm that may arise from the gastrointestinal tract and has only been recently described in the literature. Our case is unique because it is the first report of reactive nodular fibrous pseudotumor presenting as a torsed polypoid lesion and the first arising in an adolescent.

Section snippets

Case report

A previously healthy 13-year-old girl with no surgical history presented to an outside institution with a 1-day history of abdominal pain. Upon evaluation, the pain had become constant and had localized to the right lower quadrant. An abdominal ultrasound and computed tomographic (CT) scan showed free fluid in the pelvis, but the appendix was not visualized. She was transferred to our institution for further management. On examination, she was noted to be uncomfortable, with a temperature of

Discussion

Intraabdominal tumors arising in children are unusual, accounting for only 1% of all pediatric malignancies [1]. Most of these intraperitoneal tumors include non-Hodgkin lymphoma and a broad list of benign entities [2]. Reactive nodular fibrous pseudotumor is a recently described benign postinflammatory myofibroblastic lesion. It typically arises from the subserosal surface of the bowel or within the surrounding mesentery in association with local injury or inflammation. The first report

References (9)

There are more references available in the full text version of this article.
View full text
Copyright © 2012 Elsevier Inc. All rights reserved.