Case ReportHemivaginal Septum Resection in a Patient With a Rare Variant of Herlyn-Werner-Wunderlich Syndrome
Section snippets
Case Report
A 25-year-old woman, gravida 0, underwent evaluation of dysmenorrhea. Her menses, although previously regular, had become increasingly painful and longer during the past year. These symptoms remained refractory to nonsteroidal anti-inflammatory drugs and cyclic oral contraceptive pills. Her gynecologic history was significant for menarche at age 12 years. Her medical and surgical history was noncontributory. Transvaginal and transabdominal ultrasonography was performed, which revealed a uterine
Discussion
According to the American Society for Reproductive Medicine classification of müllerian duct anomalies, HWW syndrome is a class III anomaly 4, 5. The putative embryonic pathogenesis is likely due to disruption in the development of the caudal portion of 1 mesonephric duct, with secondary involvement of the ipsilateral müllerian duct 1, 6. The incidence of uterine didelphys, related to HWW syndrome, ranges between 1 in 2000 to 1 in 28 000 [2]. A complete or partial vaginal septum may occur in
Acknowledgments
We thank Beverly Eisenhuth, DO, for proofreading the manuscript.
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2019, Ginecologia y Obstetricia de MexicoObstructed hemivagina
2016, Congenital Mullerian Anomalies: Diagnosis and ManagementThe presentation and management of complex female genital malformations
2016, Human Reproduction Update
Disclosures: None declared.