Case ReportEndovascular Treatment of Aortic and Primitive Iliac Artery Aneurysms Associated With Behçet Disease
Introduction
Behçet disease (first described in 1937) is an inflammatory condition of unknown cause, which belongs to the vasculitis group. Its diagnosis is clinical and is made on the basis of three criteria, oral ulcers, genital ulcers, and uveitis.1 The cardiovascular system is affected in 25–35% patients, representing the leading cause of death.2, 3 We report the case of a patient presenting with vascular complications of Behçet disease, with an aneurysm of the infrarenal aorta and an aneurysm of the right iliac artery, which we treated successfully using an endovascular approach.
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Case Report
A 42-year-old female, Caucasian patient was hospitalized at our institution in August 2010 for pain in her lower back and left iliac fossa, lasting for several weeks. Abdominal ultrasound showed a saccular aneurysm of 15 mm × 18 mm on the left edge of the abdominal subrenal aorta and a saccular aneurysm of 17 mm × 18 mm of the right common iliac artery. An aortic computed tomography (CT) scan confirmed both aneurysms.
Since 1998, the patient had presented with a total of seven episodes of
Discussion
Behçet's disease usually appears between 15 and 45 years of age, with a peak at 30 years, affecting both men and women (but often more severe in men). It is more prevalent in Japan and Mediterranean Europe than elsewhere. It is a form of primary systemic vasculitis, with varied manifestations and whose evolution occurs in spurts between periods of remission. Clinical criteria have been defined by the International Study Group for Behçet's Disease4 (Table I).
The cardiovascular system is affected
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Cited by (4)
Endovascular Treatment of a Ruptured Innominate Artery Aneurysm in Behcet Disease
2016, Annals of Vascular SurgeryCitation Excerpt :The stent grafts were patent in 6 of the cases after 28 ± 20 months' follow-up. Successful endovascular treatment for branch arterial aneurysms in BD was also reported.8,9 Avoidance of direct touch on the affected arteries might have resulted in these good postoperative courses.
An aortic and femoral aneurysm revealing Behçet's disease
2015, Journal des Maladies VasculairesEndovascular treatment of aortic saccular aneurysms associated with adamantiades-behçet disease
2021, Jornal Vascular Brasileiro