Abstract
A male with a severe form of congenital nephrogenic diabetes insipidus (diuresis 10 l per day) had megaureters, megavesica, large residuum and a history of three traumatic ruptures of the megavesica and a recurrent urinary tract infection (RUTI). Hemodialysis was introduced at 41 years of age. At age of 42, he underwent a bilateral retroperitoneoscopic nephrectomy to prevent further RUTI and 8 months later transplantation of a cadaver kidney. Intermittent catheterization is necessary due to residual urine in the urinary bladder.
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Hora, M., Reischig, T., Hes, O. et al. Urological complications of congenital nephrogenic diabetes insipidus––long-term follow-up of one patient. Int Urol Nephrol 38, 531–532 (2006). https://doi.org/10.1007/s11255-006-0093-3
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DOI: https://doi.org/10.1007/s11255-006-0093-3