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Catastrophic antiphospholipid syndrome presenting with pulmonary hemorrhage: case report

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Abstract

This is a case report of catastrophic antiphospholipid syndrome (APLS) involving the rare manifestation of pulmonary hemorrhage. This rare variant of APLS is frequently life threatening despite medical therapy. The pathogenesis of pulmonary hemorrhage in catastrophic APLS remains incompletely understood. The optimal approach to managing pulmonary hemorrhage in the setting of catastrophic APLS is still unclear, however this case report demonstrates the success of combination therapy with anticoagulation, corticosteroids and plasma exchange.

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Authors and Affiliations

  1. The University of British Columbia, Vancouver, BC, Canada

    Tony Wan & Peter Tsang

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  1. Tony Wan
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  2. Peter Tsang
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Correspondence to Tony Wan.

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Wan, T., Tsang, P. Catastrophic antiphospholipid syndrome presenting with pulmonary hemorrhage: case report. J Thromb Thrombolysis 39, 68–70 (2015). https://doi.org/10.1007/s11239-014-1089-y

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  • DOI: https://doi.org/10.1007/s11239-014-1089-y

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