Abstract
Ewing’s sarcoma is a small, blue, round-cell tumor of mesenchymal origin which typically presents itself during the first and the second decades of life. Typically, it is noticed in the long bones of the limbs, pelvis, or ribs. There have been few reports worldwide with none in Pakistan of this rare phenomenon. We report here the case of a 16-year-old female diagnosed with Ewing’s sarcoma with intracranial extension abutting the temporal lobe resulting in proptosis and partial loss of vision in the left eye. The purpose of this case is to discuss the clinicoradiological presentation, microscopic description, and management of the patient.
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Acknowledgments
The authors like to thank the patient for providing consent to publish this case. We also appreciate the Radiology Department of Jinnah Postgraduate Medical Center and Agha Khan Hospital for providing the images necessary to complete this report. We also thank Muhammad Yasin Bandukda who assisted in editing this manuscript.
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All authors declare that no competing interests exist.
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Naqvi, S.H.A., Hameed, S., Naqvi, S.H.S. et al. Primary Ewing’s sarcoma of the orbit with intracranial extension abutting the temporal lobe: a rare case report. Int Ophthalmol 34, 1137–1140 (2014). https://doi.org/10.1007/s10792-014-9937-5
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DOI: https://doi.org/10.1007/s10792-014-9937-5