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Pure red cell aplasia and adult-onset Still’s disease

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Abstract

Pure red cell aplasia (PRCA) associated with adult-onset Still’s disease (AOSD) is very rare. In this report a 28-year-old woman was admitted with fever, skin rash, jaundice and anemia. She was diagnosed as having AOSD with PRCA by bone marrow examination. Treatment with high-dose prednisolone and intravenous immunoglobulin resulted in remission of the PRCA and a good response of the AOSD.

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Abbreviations

ANA:

Antinuclear antibodies

AOSD:

Adult-onset Still’s disease

PRCA:

Pure red cell aplasia

RF:

Rheumatoid factor

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Correspondence to Chang-Hee Suh.

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Chung, JW., Suh, YJ., Song, HJ. et al. Pure red cell aplasia and adult-onset Still’s disease. Clin Rheumatol 23, 368–370 (2004). https://doi.org/10.1007/s10067-004-0899-2

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  • DOI: https://doi.org/10.1007/s10067-004-0899-2

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