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Massive splenomegaly caused by cavernous hemangiomas associated with Klippel–Trenaunay syndrome: report of a case

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Abstract

The etiology of Klippel–Trenaunay syndrome (KTS) is not well understood. Although splenic involvement is very rare in KTS, life-threatening events such as spontaneous rupture of a splenic hemangioma may occur. We recently performed elective splenectomy for massive splenomegaly causing uncontrollable abdominal pain in a woman with KTS. The extracted spleen weighed 4260 g, and cavernous hemangiomas in the spleen were found to be the cause of the splenomegaly. The patient’s abdominal pain resolved after surgery and her postoperative course was uneventful, except for persistent bleeding from the bladder. This is a rare case of KTS with associated severe splenomegaly caused by hemangiomas.

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Conflict of interest

None of the authors have any conflict of interest to declare and have no financial relationship with the organization that sponsored this research.

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Authors and Affiliations

  1. Department of Surgery, The Jikei University School of Medicine, 3-25-8 Nishi-shinbashi, Minato-ku, Tokyo, 105-8461, Japan

    Takeyuki Misawa, Hiroaki Shiba, Yuki Fujiwara, Yasuro Futagawa & Katsuhiko Yanaga

  2. Department of Pathology, The Jikei University School of Medicine, 3-25-8 Nishi-shinbashi, Minato-ku, Tokyo, 105-8461, Japan

    Toru Harada & Masahiro Ikegami

Authors
  1. Takeyuki Misawa
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  2. Hiroaki Shiba
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  3. Yuki Fujiwara
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  4. Yasuro Futagawa
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  5. Toru Harada
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  6. Masahiro Ikegami
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  7. Katsuhiko Yanaga
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Correspondence to Takeyuki Misawa.

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Misawa, T., Shiba, H., Fujiwara, Y. et al. Massive splenomegaly caused by cavernous hemangiomas associated with Klippel–Trenaunay syndrome: report of a case. Surg Today 44, 197–200 (2014). https://doi.org/10.1007/s00595-013-0779-y

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  • DOI: https://doi.org/10.1007/s00595-013-0779-y

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