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Auditory manifestations of superficial hemosiderosis of the central nervous system

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Abstract

Superficial hemosiderosis of the central nervous system (SH-CNS) is a relatively rare condition caused by chronic or repeated subarachnoid bleeding. The aim of this article was to present hearing disorders related to SH-CNS, and to describe results of magnetic resonance imaging (MRI) to confirm the diagnosis. We performed a retrospective case review at a tertiary referral center. Clinical presentation, auditory manifestations and MRI findings of two patients with SH-CNS are reported. The two patients experienced bilateral sensorineural hearing loss (SNHL) that progressively worsened. MRI revealed typical aspects of SH-CNS on T2-weighted images. Progressive bilateral SNHL is the most common manifestation of SH-CNS. The otolaryngologist should be aware of this disease that can be easily diagnosed with MRI.

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Authors and Affiliations

  1. Otology–Neurotology Unit, Department of Otolaryngology Head and Neck Surgery, Fondation Adolphe de Rothschild, 25-29 rue Manin, 75019, Paris, France

    Denis Ayache, Catherine Blaivie, Asma El Kohen & Lucrecia Tosello

  2. Department of Medical Imaging, Fondation Adolphe de Rothschild, Paris, France

    Marc T. Williams

Authors
  1. Denis Ayache
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  2. Catherine Blaivie
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  3. Asma El Kohen
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  4. Lucrecia Tosello
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  5. Marc T. Williams
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Correspondence to Denis Ayache.

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Ayache, D., Blaivie, C., El Kohen, A. et al. Auditory manifestations of superficial hemosiderosis of the central nervous system. Eur Arch Otorhinolaryngol 264, 701–704 (2007). https://doi.org/10.1007/s00405-006-0238-0

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  • DOI: https://doi.org/10.1007/s00405-006-0238-0

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