Abstract
A 5-year-old female with Papillon–Lefèvre syndrome presented with renal mass. A radiological diagnosis of malignancy was made; however, partial nephrectomy revealed granulomatous disease indicative of chronic infection. Although liver abscess is an emerging complication in patient with Papillon–Lefèvre syndrome, this case represents the first renal abscess described in such patients.
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Morgan, R.D., Hannon, E. & Lakhoo, K. Renal abscess in Papillion–Lefèvre syndrome. Pediatr Surg Int 27, 1381–1383 (2011). https://doi.org/10.1007/s00383-011-2931-3
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DOI: https://doi.org/10.1007/s00383-011-2931-3