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Testis sparing surgery for steroid unresponsive testicular tumors of the congenital adrenal hyperplasia

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Abstract

The association between testicular tumors/nodules and congenital adrenal hyperplasia (CAH) has been recognized for many years. Tumors are considered to be an aberrant adrenal tissue that has descended with the testes and has become hyperplastic due to ACTH stimulation. The recommended treatment consists of increasing the glucocorticoid dose to suppress ACTH secretions. If the testicular size is not reduced after suppression therapy or a side effect of glucocorticoid dose is noted, surgical intervention should be considered. We diagnosed steroid unresponsive testicular tumors of the CAH in two patients who were treated by testicular sparing tumor enucleation. We believe that testis sparing surgery is the procedure of choice for all patients with testicular adrenal rest tumor, since it maximizes future fertility potential.

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Authors and Affiliations

  1. Pediatric Surgery Clinic, Social Security Institution Children’s Hospital, Ankara, Turkey

    Tuğrul Tiryaki & Halil Atayurt

  2. Department of Pediatric Endocrinology, Social Security Institution Dışkapı Hospital, Ankara, Turkey

    Zehra Aycan

  3. Pathology Clinic, Social Security Institution Dışkapı Hospital, Ankara, Turkey

    Sema Hücümenoğlu

  4. Atatürk Bulvarı Erciyes, Han No 109/14, Kızılay, Ankara, Turkey

    Tuğrul Tiryaki

Authors
  1. Tuğrul Tiryaki
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  2. Zehra Aycan
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  3. Sema Hücümenoğlu
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  4. Halil Atayurt
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Correspondence to Tuğrul Tiryaki.

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Tiryaki, T., Aycan, Z., Hücümenoğlu, S. et al. Testis sparing surgery for steroid unresponsive testicular tumors of the congenital adrenal hyperplasia. Ped Surgery Int 21, 853–855 (2005). https://doi.org/10.1007/s00383-005-1547-x

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  • DOI: https://doi.org/10.1007/s00383-005-1547-x

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