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Pediatric papillary tumors of the pineal region: to observe or to treat following gross total resection?

  • Case Report
  • Published:
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Abstract

Introduction

Papillary tumors of the pineal region (PTPR) are rare brain tumors characterized by frequent local recurrences. Standardized treatment strategies are not yet defined.

Case report

We present the case of a 3-year-old girl diagnosed with PTPR. Due to her young age, adjuvant radiotherapy was omitted after gross total tumor resection. Thirty-six months later, local tumor recurrence occurred. Considering the possible risks of secondary surgery, the recurrent tumor was irradiated with proton radiotherapy. Three months later, the tumor showed near-complete remission.

Discussion

Based on this experience and other pediatric case reports from the literature, local radiotherapy might be suggested also after complete tumor resection.

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Authors and Affiliations

  1. Department of Oncology, University Children’s Hospital of Zurich, Zurich, Switzerland

    Lucia Abela & Michael A. Grotzer

  2. Institute of Neuropathology, University Hospital of Zurich, Zurich, Switzerland

    Elisabeth Jane Rushing

  3. Center for Proton Therapy, Paul Scherrer Institute, Villigen, Switzerland

    Carmen Ares

  4. Department of Diagnostic Imaging, University Children’s Hospital of Zurich, Zurich, Switzerland

    Ianina Scheer

  5. Department of Neurosurgery, University Hospital of Zurich, Zurich, Switzerland

    Oliver Bozinov

  6. Department of Neurology, University Children’s Hospital of Zurich, Zurich, Switzerland

    Eugen Boltshauser

  7. University Children’s Hospital, Steinwiesstrasse 75, CH-8032, Zurich, Switzerland

    Michael A. Grotzer

Authors
  1. Lucia Abela
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  2. Elisabeth Jane Rushing
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  3. Carmen Ares
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  4. Ianina Scheer
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  5. Oliver Bozinov
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  6. Eugen Boltshauser
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  7. Michael A. Grotzer
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Corresponding author

Correspondence to Michael A. Grotzer.

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Abela, L., Rushing, E.J., Ares, C. et al. Pediatric papillary tumors of the pineal region: to observe or to treat following gross total resection?. Childs Nerv Syst 29, 307–310 (2013). https://doi.org/10.1007/s00381-012-1935-1

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  • DOI: https://doi.org/10.1007/s00381-012-1935-1

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