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Beckwith-Wiedemann syndrome and bilateral adrenal pheochromocytoma: sonography and MRI findings

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Abstract

Beckwith-Wiedemann syndrome is characterized by a group of clinical abnormalities, the most frequent of which are omphalocele, macroglossia, gigantism, neonatal hypoglycemia and umbilical hernia. The association of this syndrome with malignant tumors is well documented. We report a child with this syndrome associated with bilateral adrenal pheochromocytoma.

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Acknowledgements

We thank Johnny Acosta for his assistance with computer issues and Anelise Burmeister for her assistance in writing and proofreading the text.

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Authors and Affiliations

  1. Departamento de Radiologia, Hospital da Criança Conceição, Rua Francisco Trein, 596, Porto Alegre, RS, CEP 91350-200, Brazil

    Matteo Baldisserotto, Adriana Barcellos Peletti, Manoel Ângelo de Araújo, Ana Paula Cardoso Pertence, Marcelo Dourado Dora, Elines Oliva Maciel & Ana Maria Gaiger

  2. Rua Domingos Rubbo 348, apto 301, Porto Alegre, RS, CEP 91040-000, Brazil

    Adriana Barcellos Peletti

Authors
  1. Matteo Baldisserotto
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  2. Adriana Barcellos Peletti
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  3. Manoel Ângelo de Araújo
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  4. Ana Paula Cardoso Pertence
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  5. Marcelo Dourado Dora
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  6. Elines Oliva Maciel
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  7. Ana Maria Gaiger
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Correspondence to Adriana Barcellos Peletti.

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Baldisserotto, M., Peletti, A.B., Ângelo de Araújo, M. et al. Beckwith-Wiedemann syndrome and bilateral adrenal pheochromocytoma: sonography and MRI findings. Pediatr Radiol 35, 1132–1134 (2005). https://doi.org/10.1007/s00247-005-1518-3

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  • DOI: https://doi.org/10.1007/s00247-005-1518-3

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