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Hemangioendothelioma: A Rare Case of a Primary Intracardiac Tumor

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Abstract

Kaposiform hemangioendothelioma (KH) is a rare tumor of vascular origin that commonly affects the cutaneous tissues of the extremities. It can, however, affect the abdomen, thorax, head, or neck. Compared with juvenile hemangiomas, which tend to regress, KH tumors are locally aggressive and usually persist. Associated morbidity and mortality rates range from 12 to 30 % and typically are related to either compressive effects on surrounding vital structures or effects of the Kasabach–Merritt phenomenon [10, 11, 13]. To our knowledge, this report is the first to describe KH presenting as a primary intracardiac tumor.

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Authors and Affiliations

  1. Children’s National Medical Center, 111 Michigan Avenue, Washington, DC, 20010, USA

    Andrea Beaton, Dilip S. Nath, Christine Reyes, Richard A. Jonas & Gerard R. Martin

  2. Walter Reed National Military Medical Center, 8901 Rockville Pike, Bethesda, MD, 20889-5600, USA

    Trevor Kuttler

  3. Chest Disease Hospital, Kuwait City, Kuwait

    Ali Hassan

Authors
  1. Andrea Beaton
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  2. Trevor Kuttler
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  3. Ali Hassan
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  4. Dilip S. Nath
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  5. Christine Reyes
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  6. Richard A. Jonas
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  7. Gerard R. Martin
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Correspondence to Andrea Beaton.

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Beaton, A., Kuttler, T., Hassan, A. et al. Hemangioendothelioma: A Rare Case of a Primary Intracardiac Tumor. Pediatr Cardiol 34, 194–197 (2013). https://doi.org/10.1007/s00246-012-0280-1

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  • DOI: https://doi.org/10.1007/s00246-012-0280-1

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