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Infantile Form of Scimitar Syndrome with Contralateral Pulmonary Vein Stenosis

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Abstract

Infantile scimitar syndrome (SS) carries significant mortality. Consistent management guidelines have not been well established, and outcomes continue to be disappointing. We present our experience managing an SS patient with complex anatomy who developed stenosis of the pulmonary veins contralateral to the hypoplastic lung.

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Authors and Affiliations

  1. Department of Pediatric Cardiothoracic Surgery, The Congenital Heart Institute, Arnold Palmer Hospital for Children, Orlando, FL, 32806, USA

    I. Ricardo Argueta-Morales, Lauren C. Meador & William M. DeCampli

  2. Department of Pediatric Cardiac Catheterization, The Congenital Heart Institute, Arnold Palmer Hospital for Children, Orlando, FL, 32806, USA

    David G. Nykanen

Authors
  1. I. Ricardo Argueta-Morales
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  2. Lauren C. Meador
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  3. David G. Nykanen
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  4. William M. DeCampli
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Correspondence to William M. DeCampli.

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Argueta-Morales, I.R., Meador, L.C., Nykanen, D.G. et al. Infantile Form of Scimitar Syndrome with Contralateral Pulmonary Vein Stenosis. Pediatr Cardiol 31, 550–552 (2010). https://doi.org/10.1007/s00246-009-9630-z

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  • DOI: https://doi.org/10.1007/s00246-009-9630-z

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