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Ultrasonographic features of glomerulocystic disease in infancy: similarity to infantile polycystic kidney disease

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Abstract

Glomerulocystic kidney disease (GCD) is an unusual condition characterized pathologically by cystic dilatation of Bowman's space and the first portion of the proximal convoluted tubule. We report the serial ultrasound findings in an asymptomatic infant with GCD which were initially confused with infantile polycystic kidney disease. We emphasize the nonspecificity of ultrasonographic findings in cystic renal disease in early infancy and suggest a protocol for the diagnostic work-up of bilateral renal cystic disease in children.

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Authors and Affiliations

  1. Department of Pediatrics, The University of Tennessee, Memphis and LeBonheur Children's Medical Center, Memphis, Tennessee, USA

    F. B. Stapleton

  2. Department of Radiology, The University of Tennessee Memphis and LeBonheur Children's Medical Center, 848 Adams Avenue, 38 103, Memphis, TN, USA

    S. J. Fitch

Authors
  1. S. J. Fitch
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  2. F. B. Stapleton
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Fitch, S.J., Stapleton, F.B. Ultrasonographic features of glomerulocystic disease in infancy: similarity to infantile polycystic kidney disease. Pediatr Radiol 16, 400–402 (1986). https://doi.org/10.1007/BF02386818

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  • DOI: https://doi.org/10.1007/BF02386818

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