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Intussusception and leiomyosarcoma of the gastrointestinal tract in a pediatric patient

Case report and review of the literature

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Summary

Intestinal leiomyosarcoma is a rare tumor in infants and children; only 46 cases have been reported in the English literature. Presenting signs and symptoms include abdominal pain and gastrointestinal obstruction and bleeding. We describe a neonate with the unique presentation of ileocecal intussusception accompanying an ileal leiomyosarcoma. In contrast to adult patients, where intussusception is associated with smooth muscle tumors in 30% of cases, leiomyosarcoma and subsequent intussusception is rare in infancy and childhood. The overall prognosis for long-term survival is similar for both pediatric and adult patients with leiomyosarcoma of the intestinal tract, with a five-year survival in reported cases of 53% and 40%, respectively.

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Authors and Affiliations

  1. Combined Program in Pediatric Gastroenterology and Nutrition at Massachusetts General Hospital, The Children's Hospital and Harvard Medical School, Bartlett Extension 4th Floor, 02114, Boston, Massachusetts

    Glenn T. Furuta MD, David A. Bross MD, Daniel Doody MD &  Ronald E. Kleinman MD

  2. Division of Pediatric Surgery, Massachusetts General Hospital, Boston, Massachusetts

    Glenn T. Furuta MD, David A. Bross MD, Daniel Doody MD &  Ronald E. Kleinman MD

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  1. Glenn T. Furuta MD
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  2. David A. Bross MD
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  3. Daniel Doody MD
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  4. Ronald E. Kleinman MD
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Furuta, G.T., Bross, D.A., Doody, D. et al. Intussusception and leiomyosarcoma of the gastrointestinal tract in a pediatric patient. Digest Dis Sci 38, 1933–1937 (1993). https://doi.org/10.1007/BF01296122

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  • DOI: https://doi.org/10.1007/BF01296122

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