Abstract
Benign symmetric lipomatosis (BSL) is a rarely encountered disease first described by Brodie in 1846 [1]. Brodie’s description was that of a single patient with symmetric cervical fat deposition. It was not until 1898 that Madelung [2], in a study involving 35 patients, described a classic distribution of fat, including a cervical “horse collar” distribution. Launoise and Bensaude, in 1898 [3], in an extensive review of 65 patients gave a more complete description of the entity as being diffuse and disseminated with characteristic fatty neck deposits. Several forms of the disease have been described; however, Type I is the most common presentation, with a specific fat collar composed of tissue that accumulates in the upper back and neck (Fig. 50.1). This form typically affects middle-aged men of Mediterranean heritage. Cosmetic deformity and limitation of mobility due to swelling of the neck are usually the first presentations of lipomatosis [4]. More advanced deposits of fat can cause extrathoracic airway obstruction and dysphagia. Sixty to ninety percent of patients with Type I BSL have a strong history of alcohol abuse and dependence [5].
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Sclafani, A.P., Rosenstein, K., Rousso, J.J. (2010). Treatment Options in Benign Symmetric Lipomatosis. In: Shiffman, M., Di Giuseppe, A. (eds) Body Contouring. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-02639-3_50
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