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Quadricuspid aortic valve associated with aortic stenosis and regurgitation: report of a case and a review of the literature

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Abstract

Quadricuspid aortic valve (QAV) is a rare congenital heart valve disease, and more than half of QAV patients have severe aortic regurgitation (AR). We describe the case of a 66-year-old woman with QAV detected by transthoracic echocardiography during a medical checkup. Doppler echocardiographic examination showed mild aortic stenosis and mild AR. The patient has been under routine medical review without medication therapy. At follow-up echocardiographic examinations over a 4-year period, no significant changes in severity of aortic stenosis or AR were found. The clinical and functional characteristics of 192 cases of QAV were reviewed. The functional status of the QAV was known in 144 cases; of these, only 13 (9%) had both aortic stenosis and AR.

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Authors and Affiliations

  1. Second Department of Internal Medicine, Sapporo Medical University School of Medicine, Sapporo, Japan

    Yuka YAMAGISHI, Kazufumi TSUCHIHASHI, Shigeyuki SAITOH, Tetsuji MIURA, Nobuyuki URA & Kazuaki SHIMAMOTO

  2. Department of Diagnostic Ultrasound and Medical Electronics, Sapporo Medical University School of Medicine, South-1, West-16, Chuo-ku, Sapporo, 060-8543, Japan

    Satoshi YUDA

Authors
  1. Yuka YAMAGISHI
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  2. Satoshi YUDA
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  3. Kazufumi TSUCHIHASHI
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  4. Shigeyuki SAITOH
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  5. Tetsuji MIURA
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  6. Nobuyuki URA
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  7. Kazuaki SHIMAMOTO
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Correspondence to Satoshi YUDA.

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YAMAGISHI, Y., YUDA, S., TSUCHIHASHI, K. et al. Quadricuspid aortic valve associated with aortic stenosis and regurgitation: report of a case and a review of the literature. J Med Ultrasonics 34, 197–200 (2007). https://doi.org/10.1007/s10396-007-0148-9

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  • DOI: https://doi.org/10.1007/s10396-007-0148-9

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