Full PapersMyogenic Cell Lines Derived from Transgenic Mice Carrying a Thermolabile T Antigen: A Model System for the Derivation of Tissue-Specific and Mutation-Specific Cell Lines
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The mitochondrial adenine nucleotide transporters in myogenesis
2022, Free Radical Biology and MedicineMorpholino Oligomer-Induced Dystrophin Isoforms to Map the Functional Domains in the Dystrophin Protein
2020, Molecular Therapy Nucleic AcidsCitation Excerpt :Figure 1B shows that most of the dystrophin structures encoded by the distal third of the DMD gene are essential for assembly of the dystrophin-glycoprotein complex and contain important domains such as the coiled-coil domains that interact with dystrobrevin, the syntrophin binding domain, the WW domain, the ZZ domain, and the EF-hands for the direct stabilization of β-dystroglycan within the sarcolemma.15 H2K mdx myogenic cells16 were transfected with peptide-conjugated PMOs (PPMOs) at an equal oligomer ratio for preparations to skip exons 23+58+59 or exons 23+70, and the ratio of compounds to skip exons 23+56+57 was 5:4:6. The PMO sequences are shown in Table S2 and were chosen after in vitro screening outlined in Table S3 and Figure S1.
Dystrophic mdx mouse myoblasts exhibit elevated ATP/UTP-evoked metabotropic purinergic responses and alterations in calcium signalling
2019, Biochimica et Biophysica Acta - Molecular Basis of Disease
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